Abstract
Granulomatosis with polyangiitis (GPA) is necrotising vasculitis of small and medium sized blood vessels. GPA typically affects the upper/lower respiratory system and kidneys. Gastrointestinal system involvement is rarely seen. In the present paper, we report a case of small intestinal perforation as a presenting clinical manifestation in a patient with systemic GPA. The patient initially underwent surgical repair, and than achieved remission with methylprednisolone and cyclophosphamide.
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Corresponding Author
Firdevs ULUTAŞ
Department of Rheumatology, Pamukkale University Faculty of Medicine, Denizli, TURKEY
DOI: https://dx.doi.org/10.18535/jmscr/v8i7.97
