Abstract
Eosinophilic granulomatosis with polyangiitis (EGPA) is an anti neutrophil cytoplasmic antibody related small vessel vasculitis which occurs exclusively in patients with asthma and eosinophilia. Vessel inflammation and eosinophilic infiltration leads to organ damage with high incidence of neurological involvement. We report a 58 year old patient who presented with rapidly ascending weakness with hyporeflexia mimicking Guillain Barre syndrome (GBS) clinically. A history of bronchial asthma, peripheral eosinophilia and eosinophilic infiltrates in sural nerve biopsy confirmed it to be a case of EGPA. He was treated with methylprednisolone and cyclophosphamide and had good response after completion of treatment. This case highlights the rare presentation of EGPA as GBS like polyneuropathy.
Keywords: Acute polyneuropathy, Guillain Barre Syndrome, Eosinophilic Granulomatosis with Polyangiitis, Churg Strauss syndrome.
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Corresponding Author
Dr Kamalasanan. C.G
Additional Professor, Department of Internal Medicine, Government Medical College, Calicut, Kerala, India, 673008
Email: This email address is being protected from spambots. You need JavaScript enabled to view it., Mob: 9847095038
DOI: https://dx.doi.org/10.18535/jmscr/v7i1.170
