Abstract
Gonadoblastomas are rare tumors frequently appearing in the dysgenetic gonads with Y chromosome anomaly. We reported a case of gonadoblastoma in young female of age 16 years, admitted to our hospital for evaluation of early onset secondary amenorrhea since six month. Pubertal development was Tanner stage 3 and had normal 46XX karyotype. MRI Pelvis was suggestive of ovarian endometriomas. She underwent bilateral prophylactic gonadectomy. Pathological assessment found streak ovary with gonadoblastoma and foci of dysgerminoma component with extensive areas of calcification. The prophylactic gonadectomy is needed if patient carry Y chromosome or malignant components like dysgerminoma.
Keywords: Gonadoblastoma, dysgerminoma, calcification, karyotype
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Corresponding Author
Dr. Sushma Bharti MD
Address: Flat no 1202, B - Wing, Mangaldeep Apartment, In front of Pal Balaji Temple, Pal Road, Jodhpur, Rajasthan 342001, India
DOI: https://dx.doi.org/10.18535/jmscr/v6i9.164
