Abstract
Introduction: Fibro-osseous lesions are a diverse group of bone disorders with fibrous dysplasia and ossifying fibroma as the major entities. They are extremely slow growing tumors that share overlapping clinical, radiographic and histopathologic features and demonstrate a wide range of biological behaviour.
Aim: To evaluate the clinical characteristics and management of patients with fibro-osseous lesions of the cranio-facial region.
Patients and Method: All the patients presenting with the fibro-osseous lesions of the head and neck region in the department of Otorhinolaryngology of Indira Gandhi Institute of Medical Sciences from 2012 to 2015 were included in this study.
Results: A total of 10 patients were diagnosed with fibro-osseous lesions of cranio-facial region. Fibrous dysplasia was seen in 6 cases and ossifying fibroma in 4. 2 of the cases had extensive craniofacial involvement including maxilla, skull base with intracranial expansion. There was involvement of sphenoid in 3 cases, 4 cases involved maxilla and 7 cases had mandibular or the temporo-mandibular joint involvement. The most common presentation was a progressive painless swelling over face with facial asymmetry. All cases were managed surgically with complete or limited resection depending on the extent of disease and vigilant followup thereafter for any recurrence.
Conclusions: Fibro-osseous lesions are a group of slow growing benign tumors with overlapping clinical, radiological and microscopic features. However their disease course is so variable that the treatment needs to be individualized. Extensive treatment is preferred to prevent recurrence, we suggest a more conservative approach of maximum resection with minimum morbidity to be the goal of surgery for huge lesions.
Keywords: Maxillofacial, ossifying fibroma,fibrous dysplasia, mandible, cemento-ossifying.
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Corresponding Author
Singh Rakesh Kumar
Professor and Head, Department of Otorhinolaryngology, Indira Gandhi Institute of Medical Sciences, Sheikhpura, Patna, India, Zip code: 800014
Email: This email address is being protected from spambots. You need JavaScript enabled to view it., Mobile: +91 7781912005
DOI: https://dx.doi.org/10.18535/jmscr/v6i6.190
