Title: RHUPUS Syndrome in an 11 yr Old Child: A Rare Case Report
Authors: Sunil Ku Agarwalla, Poonam Agrawal, B. Maheshwar Rao, Ashok Nanda, Rina Meher
DOI: https://dx.doi.org/10.18535/jmscr/v6i3.212
Abstract
Systemic lupus erythematosus (SLE) is a multisystem disease characterized by loss of self tolerance resulting in development of auto antibodies and formation of immune complexes. Multiple organ involvement can be seen with renal and neurological involvement carrying the worst prognosis. Overlap of JIA and JSLE is a rare clinical condition in children which has been described as an entity known as RHUPUS syndrome. Prevalence of this disorder in JSLE is 2.5% [9]. In this paper we report a case of RHUPUS syndrome in an 11yr old child with clinical features of JIA in the initial presentation and eventually turned out to be a case of SLE.
Keywords: RHUPUS syndrome, Systemic lupus erythematosus, Juvenile idiopathic arthritis.
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