Abstract
Objective: to document the clinic epidemiological profile of children with hemophilia in south Kerala.
Methods: observational prospective follow up study.60 simultaneous children who attended SAT hemophilia clinic were included in the study. Data collected using predesigned questionnaire and clinical assessment. The variables include type of hemophilia, factor level, age of first bleed, type of first bleed, types of past bleeding, family history etc. inhibitor screening was done in each patient.
Results: 60 children were included in the study. Majority were found to be hemophilia A& out of them majority are severe. Most of them presented in the first half of infancy with skin and subcutaneous bleeding as the most common presentation. Only 30 % give positive family history. Only 4 of them were inhibitor positive.
Keywords: Hemophilia A and B, Inhibitors.
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DOI: https://dx.doi.org/10.18535/jmscr/v5i4.74
