Title: Pediatric Intusseption caused by Peutz Jeghers Polyp: A Case Report
Authors: Vishnu Swaroop Shrivastava, Aarti Dhatwalia, Sarita Asotra, Rajkumar
DOI: https://dx.doi.org/10.18535/jmscr/v11i12.12
Abstract
Small bowel intussusception is a rare yet significant clinical condition that can lead to various complications, particularly in the pediatric population. Here, we present a case report of a 6-year-old male child with jejunojejunal intussusception caused by multiple Peutz-Jeghers-type hamartomatous polyps in the small intestine.
The patient presented with persistent abdominal pain and vomiting, leading to the diagnosis of intussusception in the left hypochondrium. An exploratory laparotomy revealed jejunojejunal intussusception, which was manually reduced. Histopathological examination of the resected segment confirmed the presence of hamartomatous polyps with distinct histological features characteristic of Peutz-Jeghers polyps.
The distinction between Peutz-Jeghers syndrome and solitary Peutz-Jeghers-type hamartomatous polyps remains a subject of debate, especially in cases lacking mucocutaneous pigmentation and a positive family history. We discuss the complexities in defining this clinical entity and emphasize the significance of histopathological examination for accurate diagnosis.
Our case highlights the importance of considering rare pathologies in the absence of classical clinical features or positive family history, emphasizing the role of histopathology in confirming the diagnosis of Peutz-Jeghers-type polyps. Small bowel intussusception should prompt thorough evaluation, especially in pediatric cases, to prevent complications and ensure timely management.
Keywords: Intussusception, Polyp, Peutz-Jeghers polyp.
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