Cantrell’s Pentalogy is a rare congenital malformation consisting of supraumbilical abdominal defect, defect in lower part of sternum, agenesis of anterior portion of diaphragm, ectopiscordis and an intra cardiac defect. Hereby, we are reporting a case of Incomplete Pentalogy of Cantrell with, ectopiacordis, with absent pericardium, gastroschisis and Craniorachischisis.

Keywords: Pentalogy, Cantrell, ectopiacordis, Craniorachischisis.

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Dr Anjali Saji

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