Title: Ovarian Steroid Cell Tumor in a 3 year old Female: A Case Report
Authors: Dr Bismilla Mansuri, Dr Subhash Valinjkar, Dr Isha Deshmukh, Dr Neha Mathew
DOI: https://dx.doi.org/10.18535/jmscr/v7i10.148
Abstract
Steroid cell tumors [SCT] are particularly rare ovarian sex cord-stromal tumors which comprise less than 0.1% of all ovarian tumors. Theses tumors are uncommon in patients prior to puberty without atypical syndromes. We herein present a case of 3 year old female patient who presented with early onset of thelarche, pubic and axillary hair since 6 months and early onset of menarche since 2 months. USG and CECT abdomen and pelvis done which is suggestive of large well defined solid-cystic abdomino-pelvic lesion [5.4 × 6.6 × 7.7cm] noted in right adnexa. Patient underwent laparoscopic assisted right ovarian mass excision and the histopathological examination revealed an ovarian steroid cell tumor and/or leydig cell tumor. Immunohistochemistry confirmed it to be steroid cell tumor. On follow-up patient showed improvement with regression of symptoms.
Keywords: Ovarian tumor, Steroid cell tumor, Thelarche, Menarche
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