Title: Sternal Rhabdomyosarcoma Presenting As Generalised Seropositive Myasthenia Gravis
Authors: Vinit Suri, Mohit Kalangi Venkata Naga, Swapnil Jain, Kunal Suri
DOI: https://dx.doi.org/10.18535/jmscr/v7i9.104
Abstract
We report a 43 year old male patient who presented with pure motor generalised predominantly proximal quadriparesis with true fatigability, binocular diplopia, fatigable ptosis, dysarthria with mild hypernasality and dysphagia of 2 weeks duration with painless enlargement of a pre- existing sternal swelling, which was diagnosed as enchondroma previously. Repetitive nerve stimulation test confirmed the clinical diagnosis of Myasthenia gravis and acetylcholine receptor antibody was positive. Chest CT scan detected an anterior mediastinal mass which on histopathological examination revealed a pleomorphic rhabdomyosarcoma. We report this rare association of Myasthenia gravis being a presenting manifestation of pleomorphic rhabdomyosarcoma.
Keywords: Myasthenia Gravis, Seropositive, Rhabdomyosarcoma.
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