Title: A Rare Case of Craniofacial Fibrous Dysplasia
Authors: Dr Shreyansh P. Sutaria, Dr Deep Shah, Dr Bhagyashree Dave, Dr Pritesh B. Ruparelia
DOI: https://dx.doi.org/10.18535/jmscr/v6i12.172
Abstract
Craniofacial fibrous dysplasia is rare form of fibrous dysplasia. It can have devastating complications depending on which ostia are involved. Here we present the rare case of craniofacial fibrous dysplasia and highlighting clinical and radiological picture including CT scan images showing exclusive involvement of craniofacial bones. There is no universal treatment option for such disease rather than wait & watch. Presented case has been managed by riseronic acid & bisphophonate with no surgical intervention as patient’s growth was not completed. Significant reduction in serum alkaline phosphatase level & reformation of buccal cortical plate defect reported with said medical management.
Keywords: Fibrous dysplasia, monostotic, polyostotic, craniofacial.
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