Abstract
Introduction
Sickle Cell disease (SCD) is a disabling condition usually arising from inheritance, carries a turbulent lifespan with occult or overt manifestations of its complications. These complications may at times calls for an emergency management of its complications. Vaso occlusive crisis in sickle cell anemia is responsive for majority of surgical complications like chronic leg ulcer, priapism, osteomyelitis, splenomegaly, acute abdominal pain, cholecystitis. With these pathology the sickle cell disease patients present before the surgeons, it can affect any part of the body & one of the most common and early organ to be affected in SCD is Spleen .Spleen can over functions resulted in fall in all blood component1, in its milder and usually more chronic form as hypersleenism. Spleenectomy is done for varities of reasons including acute spleenic sequestration crisis hyperspleenism, Spleenic abscess2,5-8. Spleenectomy may be done either open & laparascopic method3,4. Lap. splneectomy is safe & effective10. There is also quantitative improvement in blood indices such as Hb%, Plt. count, mcv etc in post spleenectomy 9 & with improvement of immunization & penicillin prophylaxis ,the relative risk from removal of spleen have probably decreased11 .it is commonly in larged in 1st decade of life. spleenectomy in SCD patient with hyperspleenism to be beneficial in decreasing their transfusion requirement & discomfort from mechanical pressure of in larged spleen
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Corresponding Author
Dr A. K. Behera
Assistant Professor, Department of General Surgery, VIMSAR, Burla, Odisha
Contact No. 9437303084, Email: amar_behera@yahoo.co.in