Title: Idiopathic Pulmonary Hypertension and Congenital Hypothyroidism: A Rare Case Report
Authors: Prof. Dr M.Senthilvelan, Dr S.Senthilkumar, Dr H.Resveen, Dr P.Suganya, Dr Jayaram Kosalram, Dr D.Kanagaraj, Dr G.Sivachandran, Dr G.Arulvenkatesh
DOI: http://dx.doi.org/10.18535/jmscr/v4i9.25
Abstract
Idiopathic pulmonary artery hypertension (IPAH) is a rare, progressive, debilitating and fatal disease of unknown etiology. Congenital hypothyroidism is a relatively common condition, and longstanding thyroid dysfunction has been reported as a cause for IPAH. We report a case of 20 year old female patient presented with features suggestive of congenital hypothyroidism, she was found to have severe primary pulmonary hypertension and was started on treatment. The possible mechanism of pulmonary hypertension in this patient is discussed in this case report.
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Corresponding Author
Prof. Dr M.Senthilvelan
Senior Professor
Rajah Muthiah Medical College
