Abstract
Background: Synovial sarcoma is typically an aggressive malignant tumor of soft tissues, usually in the extremities but rare in head and neck region. They are called Synovial sarcoma because of their histologic resemblance to the synovium, but they do not involve a synovial structure and are believed to originate from pluripotent mesenchymal cells.
Case Presentation: We report a case of a 23-Year old male who had a complaint of swelling over left chin region previously operated in 2015 and diagnosed as spindle cell sarcoma of floor of mouth which was low-grade, now presented with recurrent swelling over floor of mouth so the patient underwent surgical intervention for the same in September 2021 at our institute and diagnosed by immunohistochemistry as recurrent synovial sarcoma of floor of mouth, then the patient was referred to our radiation oncology department for adjuvant treatment.
Conclusion: Synovial Sarcoma is rare in the oral cavity, which is slow growing and aggressive in nature. Misdiagnosis results in the delay of diagnosis and treatment of Synovial Sarcoma. Immunohistochemistry analysis might be the most important tool to confirm the diagnosis of Synovial Sarcoma. Treatment should involve wide local excision followed by adjuvant Radiotherapy depending on patient-specific factors. Lung is the most common site of metastasis.
Keywords: Recurrent Synovial Sarcoma, Immunohistochemistry, Radiation, Lung metastasis.
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Corresponding Author
Dr Krishna Prajapati
Department of Radiation Oncology, the Gujarat Cancer and Research Institute, Ahmadabad, Gujarat, India
DOI: https://dx.doi.org/10.18535/jmscr/v11i1.14
