Abstract
Congenital lobar inflation (CLO) is a rare congenital pulmonary condition with prevalence of 4.5/1,00,000. It accounts for 10% of all congenital lung malformations. This commonly presents as respiratory distress mostly in neonatal period. Congenital alveolar over distension, congenital large hyperlucent lobe, and congenital lobar emphysema are other terms previously used.(1)
Here we present the case of a 4 month old male baby who presented to the Pediatric Emergency Department with severe respiratory distress. Clinically a diagnosis of Pneumonia with Pneumothorax was made but after seeing the X ray which was suggestive of a hyper Lucent, well marginated and delineated cystic shadow occupying left lower lobe, a clinical entity of Pulmonary cyst was made. This was finally diagnosed as a case of Congenital Lobar Inflation of left lower lobe. We are reporting this case because of its rarity where strong clinical suspicion and imaging tools helped in diagnosis and timely intervention.
Keywords: congenital lobar over inflation, congenital lobar emphysema, respiratory distress, pulmonary cyst.
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Corresponding Author
Dr Arpita Jalan
Junior Resident, Department of Paediatrics, M.K.C.G. Medical College & Hospital, Berhampur, Odisha
DOI: https://dx.doi.org/10.18535/jmscr/v9i7.08
