Title: Progressive Symmetric Erythrokeratoderma- A Rare Genodermatosis

Authors: Dr Ritu Rani, Dr Mudita Gupta, Dr Ghanshyam Verma, Dr Reena K Sharma

 DOI: https://dx.doi.org/10.18535/jmscr/v9i5.07

Abstract

Erythrokeratoderma are disorders of keratinization characterized by variable erythema and hyperkeratinization. They may be syndromic and non syndromic. Progressive symmetric erythrokeratodema (PSEK) and eythrokeratoderma variabilis (EKV) are the non syndromic variety of erythrokeratoderma. There are about 100 cases reported worldwide. We are describing a classical case of PSEK in a 21 year male.

References

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Corresponding Author

Dr Mudita Gupta

Assistant Professor, Department of Dermatology, IGMC, Shimla, India