Abstract

Pheochromocytomas and paragangliomas are catecholamine-producing tumors derived from the sympathetic and parasympathetic nervous system. These tumors may arise sporadically or be inherited as features of multiple endocrine neoplasia type 2, von hippel-Lindau disease, or several other pheochromocytoma-associated syndromes. The diagnosis of pheochromocytomas identifies a potentially correctable cause of hypertension, and their removal can prevent hypertensive crisis that can be lethal.The clinical presentation is variable, ranging from an adrenal incidentaloma to a hypertensive crisis with associated cerebrovascular or cardiac complications.

Keywords: PRES, Pheochromocytoma,Vonhippel Lindau.