Abstract
Optic nerve aplasia is a rare developmental anomaly consisting of absence of the optic nerve, retinal blood vessels and ganglion cells. ONA may be an isolated finding or associated with congenital ocular and non-ocular abnormalities. It has frequent association with microphthalmos and other malformations confined to the involved eye. Unilateral ONA is generally associated with normal brain development, while bilateral ONA is usually accompanied by other central nervous system (CNS) abnormalities.
Keywords: Microcornea, Enophthalmos, Magnetic resonance imaging (MRI), Optic disc, ONA, VEP.
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Corresponding Author
Dr Rahmat Ali
Associate Professor & H.O.D Ortho., Maharshi Vashishth, Autonomous Govt. Medical College, Basti (U.P.)
DOI: https://dx.doi.org/10.18535/jmscr/v7i11.106
