Abstract
Rhabdomyosarcoma (RMS) is the most common soft tissue sarcoma in children and frequently involves the head and neck region with 10% of the cases primarily involving the orbit. It is a highly malignant tumor which can be life threatening. CT and MRI are important in the evaluation of this tumor. Histologically, embryonal subtype is the commonest in children. Complete resection followed by chemotherapy and radiotherapy is the preferred treatment of choice. We report a case of Rhabdomyosarcoma of Orbit presenting with rapid proptosis of left eye in a 10 year old male child.
Keywords: RMS, child, orbit, histology, embryonal.
References
- Xu F, De Las Casas LE, Dobbs Jr LJ; Primary meningeal rhabdomyosarcoma in a child with hypomelanosis of Ito. Archives of pathology & laboratory medicine, 2000; 124(5):762-765.
- Jurdy L, Johanus HM, Bradly M, Pieters R, Mourits MP, Roel JHM. et al; Orbital Rhabdomyosarcomas A Review. Saudi Journal of Ophthalmology 2013; 27:167-175
- Karciogl, ZA, Hadjistilianou D, Rozans M, De Francesco S; Orbital rhabdomyos-arcoma. Cancer Control, 2004;11(5):328-333.
- Kaliaperumal S, Tiroumal S, Rao VA; Orbital Rhabdomyosarcoma: A case series. Indian Journal of Cancer, 2007; 44(3):104-107
- Maurya O, Patel R, Thakur V, Singh R, Kumar M; Embryonal rhabdomyosarcoma of orbit-A case report. Indian journal of ophthalmology, 1990; 38(4): 202-204
- Rao AA, Naheedy JH, Chen JYY, Robbins SL, Ramkumar HL; A clinical update and radiologic review of pediatric orbital and ocular tumors. Journal of oncology, 2013.
- Kumar S, Perlman E, Harris CA, Raffeld M, Tsokos M; Myogenin is a specific marker for rhabdomyosarcoma: an immunohistochemical study in paraffin-embedded tissues. Modern Pathology, 2000; 13(9):988-993.
- Sebire NJ, Malone M; Myogenin and MyoD1 expression in paediatric rhabdo-myosarcomas. Journal of clinical pathology, 2003; 56(6):412-416.
- Chen SC, Bee YS, Lin MC, Sheu SJ; Extensive alveolar-type paranasal sinus and orbit rhabdomyosarcoma with intracranial invasion treated successfully. Journal of the Chinese Medical Association, 2011; 74(3):140-143.
Corresponding Author
Dr Tejal Paneria
Surat Municipal Institute of Medical Education and Research [SMIMER] Umarwada, Surat, Gujarat, India
Peamanent address: A-24 Paras nagar society, near smt I N Tekrawala high school,
Anand Mahal Road, Adajan, Surat, Gujarat, India
Contact no: 9978090099, Email: This email address is being protected from spambots. You need JavaScript enabled to view it.
DOI: https://dx.doi.org/10.18535/jmscr/v6i1.173
