Title: Clinical and Hemodynamic Characteristics of Double Chambered Right Ventricle in Adult Patients
Authors: Vishwanath Hesarur, Suresh V Patted, Sanjay Porwal, Sameer Ambar, Prasad MR
DOI: https://dx.doi.org/10.18535/jmscr/v6i1.25
Abstract
Introduction: Double chambered right ventricle (DCRV) is a rare congenital anomaly in which right ventricle (RV) is divided into two chambers by anomalous muscle band (AMB), a proximal high-pressure and distal low pressure chamber. Most of DCRV cases present during childhood, however, less commonly manifest in adulthood because of the nonspecific nature of symptoms leading to a delayed diagnosis. However, there are very few studies of DCRV in adults with regard to clinical features, hemodynamic data, treatment and prognosis, hence these are assessed in this current study.
Methods: A total of 10 adult patients (age ≥ 18 years) diagnosed as DCRV by echocardiograpy and cardiac catheterization in our hospital from January 2008 to December 2015 were included. Nine patients had a history of a known heart disease since childhood (PM-VSD) with one patient being operated at the age 9 years and one patient had isolated DCRV. Nine patients underwent surgery. Their follow-up echocardiogram showed the pressure gradient in their right ventricle was significantly decreased from 63.5 ± 14.1 mmHg preoperatively to 10.0 ± 5.0 mmHg postoperatively (p < 0.05).
Conclusion: DCRV has been reported as a rare disease in adults. Consequently, number of cases are missed and not diagnosed. Careful evaluation of DCRV by echocardiography including TEE is necessary, especially in patients with VSD. These patients should be treated surgically, because the obstruction is progressive and ends in heart failure.
Keywords: Double chambered right ventricle, Congenital, Ventricular septal defect, Echocardiography, Anomalous muscle band, cardiac catheterization, Right ventricular outflow tract.
