Abstract
Ganglioneuromas are slow growing, well differentiated neuroectodermal neoplasms, typically derived from the sympathetic ganglia and adrenal glands and more common in children. Ganglioneuromas most frequently occur in the posterior mediastinum, retroperitoneum and adrenal glands but are rare in the colon. Colonic Ganglioneuromas fall into three subgroups – polypoid ganglioneuromas, ganglioneuromatous polyposis and diffuse ganglioneuromatosis. Diffuse ganglioneuromatosis is either transmural or mucosal. Adults tend to have mucosal lesions while children can have both mucosal or transmural lesions. Here we are reporting a case of diffuse ganglioneuromatosis of colon (transmural type), clinically presenting as acute intestinal obstruction in a 79 year old male patient, which is a rare entity.
Keywords- Ganglioneuromas, Diffuse ganglioneuromatosis, colonic ganglioneuroma.
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Corresponding Author
Biparnak Haldar
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DOI: https://dx.doi.org/10.18535/jmscr/v5i11.02
