Title: Middle Aortic Syndrome (MAS) –A Rare Cause Of Hypertension In A Child with Rheumatic Heart Disease
Authors: Nasreen Ali, Sunil Kumar Agarwalla, Muhamed Shabeer, Minakhi Sahu, Nawed Momin, Jagat Shreya Satapathy, Biswajit Patanaik
DOI: https://dx.doi.org/10.18535/jmscr/v5i6.26
Abstract
The estimated prevalence of hypertension(HTN) in paediatric age group is about 2.5%.These are mostly due to secondary causes,of which renovascular causes constitute (60-70%).Middle aortic syndrome(MAS) is a rare cause of HTN.
Here we present a case of 10year old girl child, a known case of rheumatic heart disease (RHD) under treatment for carditis. She was on steroids and penicillin. She was admitted in the emergency paediatric department with complains of continued fever for 7 days. On examination the blood pressure was 180/110mm in the right arm supine position and it was thought to be steroid induced HTN. Detailed clinical examination revealed absent B\L femoral pulsation.On further investigation by MR Aortogram, a diagnosis of MAS was confirmed.MAS is a rare disease with only 200 reported cases and this is the first case report citing co-presentation of RHD and MAS.
Keywords: Renovascular cause, carditis, MR Aortogram, co-presentation of RHD and MAS
