Unusual Presentation of Dyke-Davidoff-Masson Syndrome

Title: Unusual Presentation of Dyke-Davidoff-Masson Syndrome

Authors: Dr Deepak Agrawal, Dr Manish Khandelwal, Dr Nilesh Kumar Patira

DOI: https://dx.doi.org/10.18535/jmscr/v5i5.141

Abstract

Background: Dyke-Davidoff-Masson syndrome (DDMS) is a rare disease which is clinically characterized by hemiparesis, seizures, facial asymmetry, and mental retardation. The classical radiological findings are cerebral hemiatrophy, calvarial thickening, and hyperpneumatization of the frontal sinuses. This disease is a rare entity, and it mainly presents in childhood. Adult presentation of DDMS is unusual and has been rarely reported in the medical literature. We report a Case of DDMS in a 37yr old female who presented with Tonic Clonic Seizures involving right half of the body with secondary generalization and Spastic Hemiparesis of right half of the body with facial asymmetry without mental retardation.

Material and Methods - Nil

Result - Nil

Conclusion: This case report shows an unusual presention of the rare Dyke-Davidoff-Masson syndrome (DDMS) in an adult female.

Keywords: Dyke-Davidoff-Masson syndrome, spastic hemiparesis, seizures.

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