Title: Rare Finding of Sinus Venosus type Atrial Septal Defect with Partial Anomalous Pulmonary Venous Connection presenting as Right Heart Failure and Pulmonary Hypertension in a young Adult
Authors: Dr Ashok Duggal, Dr B.S.Bal, Dr Rakesh Aggarwal
DOI: https://dx.doi.org/10.18535/jmscr/v5i2.48
Abstract
Atrial septal defects can present with pulmonary arterial hypertension in adults. The age at which symptoms appear is highly variable and is not exclusively related to the size of the shunt. Consequently, patients with ASD are at risk for developing atrial dysrhythmias with an inherent risk of thromboembolic complications. Careful assessment for these defects, and their associated pulmonary venous anomalies in patients with enlarged central pulmonary vessels, may be beneficial as surgical repair of these defects can improve outcomes. Sinus venosus defect may carry a worse prognosis than other forms of ASD and may need to be treated at a younger age with surgical closure.
