Abstract
Papillon-Lefevre Syndrome (PLS) is a rare autosomal recessive disorder first described by two French physicians, Papillon and Lefevre in 1924. Papillon-Lefevre Syndrome (PLS) is described as the association of palmar-plantar hyperkeratosis with precocious periodontal disease which results in exfoliation of primary and permanent dentitions. The majority of the teeth are lost by the age of 14 to 15 years. This case report describes the periodontal findings and dermatological findings with review of literature.
Keywords:Papillon-Lefevre syndrome, Palmoplantar hyperkeratosis, Keratodermas, Rapidly progressing periodontitis.
References
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Corresponding Author
Dr Suryakanth Malgikar*
Senior Lecturer, Department of Periodontology, KIMS Dental College,
Amalapuram – 533201, East Godavari District, Andhra Pradesh
Email: This email address is being protected from spambots. You need JavaScript enabled to view it., Mobile +91- 9591212165
DOI: http://dx.doi.org/10.18535/jmscr/v3i10.09
