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Category: Volume 09 Issue 05 May 2021
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Title: An Atypical Case of Primary Sjogren’s Syndrome Presenting as Chronic Inflammatory Demyelinating Polyradiculoneuropathy

Authors: Dr Uttayan Chakrabarti, Dr Cankatika Choudhury, Dr Vinod Chaitanya, Dr Geetika Khanna

 DOI: https://dx.doi.org/10.18535/jmscr/v9i5.08

Abstract

Sjogren’s Syndrome is a chronic autoimmune disorder affecting exocrine glands. During the course of illness, there is multi system involvement. Neurological manifestations may occur in 8.5-70% of diagnosed cases. It is well established that primary Sjogren’s Syndrome is associated with peripheral neuropathy to the tune of 10-20% although CNS involvement is much less common. These neuropathies are typically sensory or autonomic. The varieties can range from mononeuritis multiplex, distal sensory neuropathy, painful small fibre neuropathy to sensory neuronopathy. Herein, we describe an uncommon case of Sjogren’s syndrome presenting with Chronic Inflammatory Demyelinating Polyradiculoneuropathy. The former denied the hallmark sicca symptoms and was discovered on further immunological studies.

Keywords: Autoimmune disorder, Peripheral neuropathy, Sicca symptoms.

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Corresponding Author

Dr Cankatika Choudhury, MBBS,MD (Medicine)

DM Neurology trainee, Department of Neurology,Vardhman Mahavir Medical College and Safdarjung Hospital