Title: Extramedullary Plasmacytoma of the Jugular Bulb- A Rare Case Report
Authors: Dr Syeda Sarah, Anwaruddin Ahmed, Vamseedhar Annam, Sharmila P Surhonne
Introduction: Extramedullary plasmacytoma (EMP) of jugular bulb is a very rare plasma cell proliferative disorder arising outside the bone marrow.EMP represents less than 1%of head and neck malignancies. More than 90% of EMPs are diagnosed in the head and neck with the soft tissues and upper aero digestive tract being the most common sites. EMPs should be distinguished from other plasma cell dyscrasias for prognosis and treatment. There are very scarce previous documented reports on plasmacytoma arising from jugular bulb. Hence,we present here a rare case report of EMP arising from the jugular bulb masquerading as an extradural space occupying lesion
Case Report: A 56 year old man presented to our hospital with history of neck stiffness, torticollis and progressive nuchal pain since 3 months. Radiological findings identified an extradural expansile mass lesion in the left jugular foramen bulb causing bony erosion. Intraoperative squash cytology suggested a differential diagnosis of small round blue cell tumor. Surgical excision of the mass was performed and sent for histopathological evaluation, which showed features of plasmacytoma. Immunohistochemistry was positive for CD 138 confirming the diagnosis of EMP.
Keywords: Extramedullary Plasmacytoma, Squash Cytology, IHC.