Title: Sturge-Weber syndrome: A Case Report in estimating diagnostic importance of Neuroimaging

Authors: Dr Abhishek Kaushik, Dr Sachin, Dr Kirti Chaturvedy, Dr Prateek Sihag

 DOI: https://dx.doi.org/10.18535/jmscr/v7i2.58

Abstract

Sturge Weber syndrome (SWS) is a rare neurocutaneous syndrome, that is sporadic and in majority of the cases is characterized by a port wine stain.  We aimed to present a SWS patient with the history of convulsions and to draw attention towards the role of MRI and NCCT in evaluating the cases of SWS. A 6-year-old male patient presented our department for NCCT head with complaints of an episode of convulsion. At his physical examination a facial nevus was observed. He had a history of convulsions at the age of 8 months. 

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Corresponding Author

Dr Abhishek Kaushik

PG MD Resident Doctor, Dr SNMC Jodhpur Rajasthan, India