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Category: Volume 06 Issue 01 January 2018
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Title: Primary Renal Leiomyosarcoma: A Case Report

Authors: Aakanksha Singh, Preeti Diwaker, Navneet Kaur

 DOI:  https://dx.doi.org/10.18535/jmscr/v6i1.77

Abstract

Introduction

Primary sarcomas of kidney are rare tumors, which comprise 0.8% of all renal tumors. Leiomyosarcoma account for 50-60% of kidney sarcomas; followed by liposarcomas in 10-15% of cases1. They usually occur in the right kidney2. Mesenchymal tumors of the kidney lack natural barriers and hence are able to expand and present as a large abdominal lump. Sarcomas typically possess a pseudocapsule, which is often infiltrated by the tumor3. The documented biological behaviour of renal leiomyosarcoma is unpredictable which may be due to paucity of extensive literature. However, the disease is known to be associated with a poor prognosis and a high metastatic potential4.

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Corresponding Author

Dr Preeti Diwaker

Assistant Professor, Department of Pathology

UCMS & GTBH, Dilshad Garden