Title: Fibrous Dysplasia of Skull and Facial Bones: A Hospital Based Survey Based on Computed Tomography (CT) Findings
Authors: Dr Ashok Kumar Mandal, Dr Satya Prakash Shankaram, Dr Jagriti Narayan, Dr (Prof.) Gyanendra Narain Singh, Dr (Prof.) Vijay Shankar Prasad, Dr Rajiv Kumar, Dr S.N.Pathak
DOI: https://dx.doi.org/10.18535/jmscr/v5i9.57
Abstract
Introduction: Fibrous dysplasia is a benign disease characterised by a slow progressive replacement of normal bone elements with fibrous tissue. It represents a bone developmental disorder specially a defect in osteoblastic differentiation and maturation. There are two primary categories of the disease: monostotic fibrous dysplasia [70- 85%] that involves a single bone and polyostotic fibrous dysplasia [20- 30%] that involves multiple bones. In the head and neck region, craniofacial involvement in fibrous dysplasia occurs in nearly 100% of polyostotic and 30%of monostotic form.
The diagnosis is mainly based on radiological findings and the modality of treatment is mainly conservative.
Aims and Objectives: The aim of the study is to evaluate the involvement of skull and facial bone in diagnosed case of fibrous dysplasia based on CT features.
Materials and Methods: The study was carried out during the period of December 2013 to November 2015 (period of two year). 40 patients of fibrous dysplasia involving skull and craniofacial bones were included in the study.
Results and Observations: The skull and facial bones are in majority involved by polyostotic variety of fibrous dysplasia with maxilla and mandible involvement seen in majority of them.
Conclusion: skull and facial bone involvement is more common in polyostotic form than in monostotic form of fibrous dysplasia. maxilla and mandible involvement seen in majority of polyostotic variety. less common involved bone was lacrimal, temporal, vomer and inferior nasal concha
Keywords: fibrous dysplasia, temporal bone, skull, craniofacial bones, monostotic, polyostotic.
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