Title: Persistant Mullerian Duct Syndrome with Transverse Testicular Ectopia Presenting as Left Inguinal Hernia with Cryptorchidism, A Rare Presentation
Authors: Dr Javid Iqbal* MS, FMAS, FIAGES, Dr Yasmeen Kousar MBBS, DGO, Dr Sonam Gupta MBBB
DOI: https://dx.doi.org/10.18535/jmscr/v5i5.20
Abstract
Inguinal hernia and undescended testes in a patient can present with transverse testicular ectopia (TTE) and very rarely, with residual Mullerian duct structures. This is called persistent Mullerian duct syndrome (PMDS). PMDS is mostly discovered during surgery for inguinal hernia or cryptorchidism. TTE is a rare congenital anomaly in which both testes descend through a single inguinal canal. Patients with TTE present with symptoms of cryptorchidism and inguinal hernia. Herein, we reported one TTE case with PMDS. For patients with inguinal hernia and cryptorchidism associated with TTE, PMDS should be kept in mind and radiologic evaluation with ultrasonography or magnetic resonance imaging of the genitourinary system and karyotyping should be done.
Keywords: Orchiopexy, persistent Mullerian duct syndrome, transverse testicular ectopia, inguinal hernia.
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