Title: Acral Persistent Papular Mucinosis in Indian Patient: Rare Presentation with Review of Literature

Authors: Dr Amit Chauhan, Dr Mudita Gupta, Dr Anchana Gulati, Dr Pragya Gupta

 DOI:  https://dx.doi.org/10.18535/jmscr/v5i2.14

Abstract

Acral persistent papular mucinosis is a rare subtype of localized lichen myxedematosus. Presenting as acrally located bilaterally symmetric, asymptomatic papules. These lesions are ivory to flesh-coloured, 2–5mm sized papules arranged on the dorsum of the hands and extensor aspects of distal forearms and are persistent. Thirty-five cases appear to fit the proposed diagnostic criteria till this date as reported in literature. We report a 60-year-old Indian man who presented with papules on the dorsum of his hands for last six years. Histopathology revealed circumscribed area in the upper and mid reticular dermis with splaying of collagen fibers caused by mucin deposits. Deposits stained positively with alcian blue at pH 2.5. The thyroid profile was normal.

Keywords: acral, persistent, mucinosis.

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Corresponding Author

Dr Mudita Gupta

Dept of Dermatology, Venereology and Leprosy

Indira Gandhi Medical College, Shimla, Himachal Pradesh

Email: This email address is being protected from spambots. You need JavaScript enabled to view it., Ph no. 9418495747