Proximal Epithelioid Sarcoma: A Diagnostic Challenge

Title: Proximal Epithelioid Sarcoma: A Diagnostic Challenge

Authors: Dr Ajeet Kumar, Dr Guddi Rani Singh, Dr V.Choudhary, Dr Suryajit Kumar Singh, Dr Amit Kumar Sinha

DOI: https://dx.doi.org/10.18535/jmscr/v4i10.38

Abstract

Epithelioid sarcoma is an uncommon slow-growing soft tissue malignancy, associated with a high incidence of local recurrence and metastasis. We report a 30-year-old male presented with huge mass in left thigh with difficulty in walking, clinically misdiagnosed as clear cell sarcoma. Multiple nodule noted in left lung parenchyma suggestive of metastasis. Later histopathological examination and IHC confirmed the diagnosis of epithelioid sarcoma. Here we present the case because of large number of histological mimics of epithelioid sarcoma and its unusual location.

Keywords: Epithelioid sarcoma, Soft tissue sarcoma, metastasis.

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Corresponding Author

Dr Ajeet Kumar

Senior Resident, Department of Pathology, IGIMS, Patna

Department of Pathology, IGIMS, Patna, Bihar