Case Report of Symptomatic and Asymptomatic Ebstein’s Anomaly- Cardiac MR Imaging

Title: Case Report of Symptomatic and Asymptomatic Ebstein’s Anomaly- Cardiac MR Imaging

Authors: Seena CR, Janani AV, Kulasekaran N

DOI: https://dx.doi.org/10.18535/jmscr/v4i11.77

Abstract

We hereby report two cases of Ebstein’s anomaly, one of the rare congenital heart diseases accounting for only 0.5-1.0 % of congenital heart diseases with incidence of 1 in 2,10,000 live births. Ebstein’s anomaly has a wide spectrum of findings, and ages at first presentation while some patients are asymptomatic. We present a classic case of Ebstein’s anomaly in a 22-year-old female with massive right sided cardiomegaly, downward displacement of septal tricuspid leaflet, atrialization of right ventricle associated with atrial septal defect. We also present another case of Ebstein’s anomaly in a 51-year-old male who was asymptomatic. We also emphasize the role of MRI in assessing apical displacement of the septal leaflet of tricuspid valve, mobility of antero-superior and inferior tricuspid valve leaflets, quantification of tricuspid regurgitation and size of atrialized right ventricle and to assess volume.

Keywords- Ebstein’s anomaly, atrialized right ventricle, tricuspid valve.

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Corresponding Author

Dr Janani A.V.

Department of Radio-Diagnosis & Imaging, Saveetha Medical College Hospital,

Saveetha Nagar, Thandalam – 602105 Kancheepuram (Dist.), Tamil Nadu, India.

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