Title: Endolymphatic Sac Tumour: A Case Report
Authors: Dr Rosemary Raphael, Dr P V Priya, Dr S Sankar
DOI: https://dx.doi.org/10.18535/jmscr/v9i11.06
Abstract
Endolymphatic Sac tumor (ELST) is a rare skull base tumor originating from epithelium of the endolymphatic sac which can occur sporadically or in Von Hippel Lindau syndrome. This neoplasm is characterized by slow growth, local invasion and bone destruction. Histopathologyof this tumorshows papillary growth pattern with low grade nuclear features. We report a 39-year-old man who presented with recurrent skull base lesion, which was diagnosed as ELST. Because of the rarity of this lesion, it can easily be confused with other skull base and middle ear neoplasms. An accurate neuroradiological, histopathological and immunohistochemical correlation is necessary for the diagnosis of this rare neoplasm.
Keywords: Endolymphatic sac tumor, Heffner tumor, VHL syndrome.
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