Title: PHACE Syndrome: A Rare Case Study

Authors: Dr Hari Sankar T, Dr S K Pradhan, Dr C S Patra, Dr S S Mishra

 DOI: https://dx.doi.org/10.18535/jmscr/v9i1.24

Abstract

PHACE is a clinic-radiological syndrome first described by Friedon in 1996 as an infantile segmental hemangioma with other features like posterior fossa abnormalities, arteriopathy, cardiac defects and eye anomalies.

Long term outcome varies according to the severity of associated defects.

Keywords: PHACE, Hemangiomas, VSD, CoA, LASER.

References

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Corresponding Author

Dr Hari Sankar T

Junior Resident, Department of pediatrics. MKCG Medical College