Abstract
Objective: To outline the epidemiological profile and prognostic factors for Ewing's sarcoma in a rural medical college in hilly area in West Bengal
Material and Methods: The medical records of 27 patients with Ewing's sarcoma who were treated at North Bengal Medical College, Darjeeling in West Bengal in India from January2010 to December 2017, were retrospectively evaluated.
Results: Out of the the total 27 patients, commonest age group was 8-16 years. Male to female ratio was 1.25:1. Most of the patients presented with pain, swelling and alteration in gait. Involvement of appendicular skeleton particularly femur was commonest. Many patients presented with metastases. Lung was commonest site of metastases. Patients who presented at younger age, had involvement of peripheral skeleton, less bulky disease and underwent surgery along with chemotherapy and Radiotherapy did better with treatment.
Conclusion: The prognosis in cases of Ewing's sarcoma was mainly influenced by the presence of metastases at the time of diagnosis, involvement of peripheral (appendicular) skeleton, disease bulk and age.
Keywords: Ewings Sarcoma; Metastases; Prognosis.
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Corresponding Author
Subrata Chatterjee
Address-Orbit Sky View, Block-4, Flat-10C, 1/1A, Umakanta Sen Lane, Kolkata-700030, India
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DOI: https://dx.doi.org/10.18535/jmscr/v6i10.52
