Title: Peri-Genital Proliferating Trichilemmal Cyst: A Clue to Underlying Malignancy
Authors: Dr Kuldeep Verma, Dr Ghanshyam Verma, Dr G.R.Tegta, Dr Ajeet Negi, Dr Lalita Negi
DOI: https://dx.doi.org/10.18535/jmscr/v6i2.130
Abstract
Proliferating trichilemmal cyst (PTC) is an uncommon tumour arising from outer root sheath of hair follicle which frequently present over the scalp as an isolated swelling 1 to 10 cm in size. PTC is assumed to arise from trichilemmal cyst with histological hallmark of trichilemmal keratinisation. Hardly ever, PTC can endure malignant transformation at which point, it is termed as malignant proliferating trichilemmal cyst (MPTC) which has a high chance of metastasis. We report a case of PTC at exceptional site in an elderly female at peri-genital area with later evolution to cutaneous squamous cell carcinoma (SCC) and metastasized to regional lymph nodes. On further exploration an underlying carcinoma cervix was also detected. So PTC served as a clue for cutaneous as well as cervical malignancy.
Keywords: Proliferating Trichilemmal Cyst, Squamous Cell Carcinoma, Metastasis
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