Title: Orbital Rhabdomyosarcoma in a Child
Authors: Dr Tejal Paneria, Dr Manisha Shastri
DOI: https://dx.doi.org/10.18535/jmscr/v6i1.173
Abstract
Rhabdomyosarcoma (RMS) is the most common soft tissue sarcoma in children and frequently involves the head and neck region with 10% of the cases primarily involving the orbit. It is a highly malignant tumor which can be life threatening. CT and MRI are important in the evaluation of this tumor. Histologically, embryonal subtype is the commonest in children. Complete resection followed by chemotherapy and radiotherapy is the preferred treatment of choice. We report a case of Rhabdomyosarcoma of Orbit presenting with rapid proptosis of left eye in a 10 year old male child.
Keywords: RMS, child, orbit, histology, embryonal.
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