Title: Fahr's disease with Epilepsy: A Case Report

Authors: Dr Md Asif Ansari, Dr Arijit Saha, Dr Santosh Kumar

 DOI:  https://dx.doi.org/10.18535/jmscr/v5i11.23

Abstract

Fahr's disease, first described by Karl Theodor Fahr in 1930, refers to sporadic or familial idiopathic basal ganglia calcification that is associated with many neurological and psychiatric abnormalities, but may also be secondary to other diseases. Most cases present with extrapyramidal symptoms. But here we describe a case of Fahr's disease, who presented with extrapyramidal symptoms with generalized tonic clonic seizures. Computed tomography scan of brain showed bilateral calcification of cerebral hemispheres, basal ganglia and in parietal regions, due to abnormal calcium and phosphate metabolism.

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Corresponding Author

Dr Santosh Kumar

F-110, New Doctors Hostel, MGM Campus, Kishanganj, Bihar

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