Title: Immunoglobulin G4-Related Disease (IgG4-RD) Presenting as Sclerosing Cholangitis - A Radiological Case Report
Authors: Kirti Rana Chaturvedy, Navjeet Kaur, Ramanand Gehlot, Preeti Meena
DOI: https://dx.doi.org/10.18535/jmscr/v5i7.226
Abstract
Immunoglobulin G4-related disease (IgG4-RD) is a rare systemic fibro-inflammatory disorder mimicking inflammatory and neoplastic processes. Numerous extrapancreatic organs such as the bile ducts, gallbladder, kidneys, retroperitoneum, thyroid, salivary glands, lung, mediastinum, lymph nodes, and prostate may be involved, either synchronously or metachronously. This case report of a 36 year old Indian male aims to highlight the imaging spectrum of multi-organ involvement in a case of IgG4 related disease. It is important to recognize multiorgan involvement of IgG4-related sclerosing disease and be familiar with its clinical and imaging features because it demonstrates a favourable response to treatment. Our case report leads us to reflect on the necessity to take into account this disease in patients with multisystem involvement.
Keywords: Immunoglobulin G4 related disease, sclerosing cholangitis, phlebitis, thrombosis, fibrosclerosing lesion.
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