Title: Anaesthetic Considerations in Neurofibromatosis Complicated with Kyphoscoliosis and Restrictive Lung Disease
Authors: Dr Harpreet Kaur, Dr Harkomal Kaur, Dr M. Magila
DOI: https://dx.doi.org/10.18535/jmscr/v5i7.175
Abstract
Neurofibromatosis is a genetically transmitted disease arising from the nervous tissue. It is associated with widespread systemic manifestations that pose a challenging situation to the anaesthesiologist. Kyphoscoliosis is one of the musculoskeletal anomalies that present in 10% of patients with neurofibromatosis I. The present case discusses the anaesthetic considerations of a known case of NF I with associated kyphoscoliosis who was posted for surgical removal of mass from the right iliac crest and thigh under spinal anaesthesia. A thorough pre anaesthetic evaluation and workup turn out to be the cornerstone in management of such cases.
Keywords: neurofibromatosis I, plexiform neurofibroma, scoliosis, respiratory system, anaesthesia, spinal, kyphosis.
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