Title: Comprehensive Assessment of Joint Disability in Children with Hemophilia & Plan of Action for Effective Intervention
Authors: Dr Devakumar V K MBBS DCH DNB, Dr P G Hariprasad MBBS DCH DNB
DOI: https://dx.doi.org/10.18535/jmscr/v5i4.157
Abstract
Background and objectives: Permanent disability follows chronic haemophilic arthropathy. So it is important to periodically assess joint function in haemophilic children and do early intervention. There are very few studies in Kerala regarding haemophilic children and their problems especially joint function. SAT hospital is a tertiary care centre in Trivandrum catering to patients from south Kerala. Haemophilia clinic is conducted in SAT every Saturday. Objectives of the present study are to find the extent of joint disability in haemophilia patients using Haemophilia joint health score, to find the outcome after standard care in the Hemophilia clinic.
Methods: Observational Hospital level prospective follow up study at SAT Hospital, Thiruvananthapuram. Joint health was assessed using Haemophilia Joint Health Score (HJHS 2.1). After intervention HJHS 2.1 repeated at 3 monthly interval twice.
Results & Discussion: Study was conducted among 60 haemophiliac children attending SAT haemophilia clinic. Majority were haemophilia A, 86.7%. Haemophilia B constituted only 13.3 % .76.7% were having severe disease. 20.0 % moderate disease, 3.3 % having mild disease. In the study group, 27 children (45%) had haemophilic arthropathy. In 48.1%, haemophilic arthropathy developed at more than 9 years of age. There was statistically significant improvement in HJHS Score in children receiving treatment from haemophilia clinic SAT, Hospital, Thiruvananthapuram
Conclusion: In the study group, 27 children (45%) had haemophilic arthropathy. There is significant improvement in HJHS2.1 score in haemophilia patients receiving treatment and care in hemophilia clinic.
Keywords: Haemophilia; HJHS2.1; haemophilic arthropathy,
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