Title: Metastatic Angiosarcoma of Liver: A Case Report

Authors: Sapam Opendro Singh, Lalsangzuala Tochhawng, Saswade Kalpesh, Verma Nityanand, Vijayan Surya M, Th Sudhir Chandra Singh

 DOI:  https://dx.doi.org/10.18535/jmscr/v5i2.109

Abstract

Angiosarcoma is a rare malignant tumour of endothelial origin with a poor prognosis; significantly, patients with intestinal angiosarcoma who survive over 1 year after diagnosis are extraordinarily rare. This article describes the case of a 43-year-old patient with HIV infection who presented with abdominal pain of 4 months duration along with swelling in the right upper part of abdomen which had increased in severity 4 weeks prior to presentation. After a complicated diagnostic process, the diagnosis of metastatic liver angiosarcoma was made by history and imaging. We reviewed previous cases of angiosarcoma described in the English literature to determine their risk factors, diagnosis and treatment, and we found that angiosarcoma is extremely rare, especially metastatic liver angiosarcoma. To the best of our knowledge, this may be the first case of primary angiosarcoma of the large intestine with metastasis to the liver reported in the English literature.

Keywords: Large intestine, Primary angiosarcoma, Hepatic metastasis, Hepatectomy.

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Corresponding Author

Dr Lalsangzuala Tochhawng

PG Student, Department of Surgery

Regional Institute of Medical Sciences, Imphal, Manipur, INDIA