Title: A Rare Case of Oculopalatal Myoclonus

Authors: Subhasish Deb, Arvind RV, Vishal Gaikwad, Arun Agarwalla, Sumit Sarkar

 DOI:  https://dx.doi.org/10.18535/jmscr/v5i1.43

Abstract

We present a rare case of a 40 year old female who suffered a pontine haemorrhage due to uncontrolled hypertension and a year later, was found to have oculopalatal myoclonus.Oculopalatal myoclonus is characterized by rhythmic pendular vertical eye movements associated with synchronous contraction of the soft palate. It produces intractable oscilopsia and normally is due to brain stem haemorrhage. The site of the lesion usually is in the triangle of GuillianMollaret. We would like to report this case due to its rarity. Most of these patients do no complain of dysphagia or dyspnonia and should be counselled about that fact that they can lead a normal life despite having anoculopalatal myoclonus.

Keywords-oculopalatal myoclonus, guillianmollaret triangle.

References

1.      1.      Leigh RJ, Zee DS. The neurology of eye movements. 3rd ed. New York: Oxford University Press, 1999.

2.      Talks SJ, Elston JS. Oculopalatal myoclonus: eye movement studies, MRI findings and the difficulty of treatment. Eye 1997;11:19–24

3.      Matsuo F, Ajax ET. Palatal myoclonus and denervation supersensitivity in the central nervous system. Ann Neurol 1979;5:72–8.

4.      Guillain G, Mollaret P: Deuxcas de myocloniessynchrones et rythméesvélo-pharyngo-laryngo-oculo-diaphragmatiques: le problèmeanatomique et physio-pathologique de ce syndrome. Rev Neurol (Paris) 1931;2:545–566.

5.      Mugnaini E, Nelson BJ. Corticotrophin-releasing factor (CRF) in the olivo-cerebellar system and the feline olivary hypertrophy. EBR Series 17, 187-197, 1989

6.      Deuschel G, Mischke G, Schenck E, Schulte-monting J, Lucking CH. Symptomatic and essential rhythmic palatal myoclonus. Brain (1990), 1645-1672

7.      Leigh, R. J., T. H. Burnstine, R. L. Ruff, et al. (1991). "Effect of anticholinergic agents upon acquired nystagmus: a double-blind study of trihexyphenidyl and tridihexethyl chloride." Neurology41(11): 1737-41.

Corresponding Author

Subhasish Deb

Junior Resident Hostel, Room 5, Burdwan Medical College, Burdwan- 713104, West Bengal

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