Title: Glomus Tumour-A Rare Presentation - Case Report

Authors: Dr Verranna Kotrashetti, Dr Vijay Sonawane, Dr Kapil Bainade, Dr Abir Lal Nath

 DOI:  http://dx.doi.org/10.18535/jmscr/v3i12.08

Abstract

Introduction: Glomus jugulare tumors are rare, slow-growing, hypervascular tumors that arise within thejugular foramen of the temporal bone. They are included in a group of tumors referred to as paragangliomas, whichoccur at various sites and include carotid body, glomus vagale, and glomus tympanicum tumors.

Case Presentation: A 4 year female child born to Non consangious parents presented with deviation of angle of mouth to the left since 2 month with drooping of eyelids and severe pain in the left premastoid region.Preliminary examination  revealed purulent discharge which was foul smelling and ptosis. Child developed altered sensorium with facial weakness and was shifted in PICU and MRI brain and HRCT temporal bone s/o GLOMUS tumour.Managed with antibiotics.

Conclusion: Glomus tumors are benign, slow growing tumors originating from paraganglionic tissue, mostly located at the carotid bifurcation, jugular foramen, cervical portion vagus nerve, and middle ear cavity. Radiotherapy is treatment of choice for patients with intracranial extension, and patients with bilateral and multiple tumors, or patients who are inoperable.

Keywords: Glomus Tumour(GT)

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Corresponding Author

Dr Abir Lal Nath

MBBS, PG Student MD Paediatrics 2nd Year

Department of Paediatrics, DY Patil Medical College Nerul Navi Mumbai